Key Results
Top hypothesisSpontaneous Misfolding
P(spontaneous)0.427
P(proteostasis)0.219
P(somatic mutation)0.197
Best multi-hit model3 hits
MM relative risk1.75x
sCJD incidence1.5/million/yr
Etiological Model Posteriors
Codon 129 Genotype Risk
Multi-Hit Model Comparison